Gorlin-Goltz Syndrome - An Unusual Case Report


  • Sathyabama University, Department of Oral Pathology, Dental College and Hospital, Chennai, Tamil Nadu, India
  • Tamil Nadu Government Dental College & Hospital, Department of Prosthodontics, Chennai, Tamil Nadu, India
  • D Care Multispecialty Dental Clinic, Department of Oral Pathology, Chennai, Tamil Nadu, India


Gorlin-Goltz syndrome is an uncommon autosomal dominant disorder manifesting as a multisystemic disease. Keratocystic odontogenic tumor (KCOT) is considered as the most consistent feature of this syndrome. Dentists play a key role in making early diagnosis of this syndrome. Here we present a case of Gorlin- Goltz syndrome identified by multiple multilocular radiolucencies in the mandible. A review of literature of different diagnostic criteria for Gorlin-Goltz syndrome is also discussed.


Gorlin-Goltz Syndrome, Nevoid Basal Cell Carcinoma Syndrome, Keratocystic Odontogenic Tumor, Multilocular Radiolucency.

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